Test Bank Chapter 22 Case Study Duchenne Muscular Dystrophy

Chapter 22. Case Study: Duchenne Muscular Dystrophy

Multiple Choice

Identify the choice that best completes the statement or answers the question.

1. Duchenne muscular dystrophy is an:
   1. autosomal recessive disorder.
   2. autosomal dominant disorder.
   3. X-linked recessive disorder.
   4. acquired disorder.
2. Among male births, the incidence of Duchenne muscular dystrophy is variably reported as 1 in:
   1. 1,000.
   2. 3,500.
   3. 7,250.
   4. 10,000.

1. Duchenne muscular dystrophy is associated with an absence of:
   1. dystrophin.
   2. red blood cells.
   3. white blood cells.
   4. platelets.
2. Boys with Duchenne muscular dystrophy tend to use the Gowers’ maneuver to rise from the floor because of weakness in:
   1. hip flexors, extensors, and abductors.
   2. hip flexors and extensors, and knee extensors.
   3. hip extensors, knee flexors and extensors.
   4. hip extensors and abductors and knee extensors.
3. Development of contractures in boys with Duchenne muscular dystrophy has been documented to occur in which sequence?
   1. Heel cords, IT band/TFL, hip flexors
   2. Hip flexors, knee flexors, elbow flexors
   3. Heel cords, knee flexors, hip flexors
   4. Hip flexors, elbow flexors, wrist flexors
4. In boys with Duchenne muscular dystrophy, muscle weakness appears first in the:
   1. cardiac and respiratory muscles.
   2. ankle plantar flexors, facial muscles, muscles involved in speech, and sphincters.
   3. neck flexors, abdominal muscles, hip extensors and abductors, and knee extensors.
   4. finger flexors and extensors, wrist and elbow flexors.
5. Physical therapy intervention for young boys with Duchenne muscular dystrophy should include:
   1. rigorous progressive resistive exercises.
   2. daily stretching and promotion of regular age-appropriate physical activity.
   3. gait training with posture-control walker.
   4. functional electric stimulation.
6. As Duchenne muscular dystrophy progresses, the greatest life-threatening concerns are:
   1. cerebral hemorrhage and seizures.
   2. pulmonary infections and seizures.
   3. cerebral thrombosis and seizures.
   4. neoplasms and cardiac arrest.
7. A pharmacological intervention that can prolong ambulation for boys with Duchenne muscular dystrophy is:
   1. nonsteroidal antiinflammatory medications.
   2. chemotherapy.
   3. antimalarials.
   4. corticosteroids.
8. For boys with Duchenne muscular dystrophy, function can be maintained using all of the following interventions except:
   1. corticosteroids.
   2. scoliosis surgery.
   3. aggressive strengthening exercises.
   4. knee-ankle-foot orthoses.
9. A functional test that is used to document disease progression in Duchenne muscular Dystrophy is the
10. PedsQL.
11. North Star Ambulatory Assessment.
12. Hammersmith Functional Motor Scale.
13. Bayley Scale of Infant Motor Development.

True/False

Indicate whether the statement is true or false.

1. Some boys who are delayed in their development of ambulation and speech are later diagnosed with Duchenne muscular dystrophy.
2. The validity, reliability, and sensitivity of manual muscle testing, range of motion testing, and timed function tests have been established in patients with Duchenne muscular dystrophy.
3. Surgical correction of scoliosis and spinal stabilization are considered cosmetic procedures that do not improve function or longevity for boys with Duchenne muscular dystrophy.
4. Corticosteroids have been found to improve muscle mass and function in the short term, but prolonged use does not affect outcomes in boys with Duchenne muscular dystrophy.
5. Duchenne muscular dystrophy affects skeletal muscle, cardiac muscle, and smooth muscle of the gastrointestinal tract but is not associated with learning disabilities.
6. Timed function tests of supine to stand, time to traverse 30 feet, and time to climb 4 stairs are reliable and sensitive measures of function in boys with Duchenne muscular dystrophy.

Chapter 22